Diseases Of Bone And Joints Question And Answers

Diseases Of Bone And Joints Question And Answers

Question 1. Write short note on cleidocranial dysplasia

Answer. It is also called as cleidocraniodysostosis or “Marie and Santon disease.”

Cleidocraniodysostosis Etiology

• It appears as true dominant Mendelian characteristic.
• It is transmitted as an autosomal dominant trait with complete penetrance and variable expressivity.

bone and joint diseases

Oral Manifestation Of Cleidocranial Dysplasia

• Maxilla and paranasal air sinuses are underdeveloped resulting in maxillary micrognathia.
• Maxilla is underdeveloped in relation to mandible.
• There is prolonged retention of primary dentition.
• There is complete absence of cementum.
• Disorganization of developing permanent dentition.
• There is presence of supernumerary teeth usually in anterior region.
• High narrow arched palate and cleft palate is common.
• Roots of teeth are often short and thinner than the normal.
• The crown may be pittd as a result of enamel hypoplasia.

diseases of bones and joints

Read And Learn More: Oral Pathology Question And Answers

Clinical Features Of Cleidocranial Dysplasia

• There is complete absence of clavicle.
• It primarily affects skull, clavicle, and dentition.

Treatment For Cleidocranial Dysplasia

• Not specific
• Dental care should be taken.